Sarcoma / 2020 / Article / Tab 2 / Research Article
Clinical Characteristics, Management, and Outcomes of 19 Nonpediatric Patients with Desmoplastic Small Round Cell Tumor: A Cohort of Brazilian Patients Treatment modality Number of patients (%) Chemotherapy Neoadjuvant 9 (47) Palliative 10 (53) First line (n = 19) VAC/IE 7 (37) VAC 3 (16) VAI 3 (16) VAC/ICE 1 (5) AI 1 (5) Carboplatin/ifosfamide/etoposide 1 (5) Carboplatin/paclitaxel/bevacizumab 1 (5) Carboplatin/paclitaxel 1 (5) Cisplatin/etoposide 1 (5) Second line (n = 13) IE 3 (23) VAC 2 (15) Pazopanib 2 (15) High-dose ifosfamide 1 (7) Dacarbazine/gemcitabine 1 (7) Topotecan 1 (7) Irinotecan 1 (7) Sunitinib 1 (7) FOLFOX 1 (7) Third line (n = 11) Gemcitabine/docetaxel 3 (27) Irinotecan 2 (18) Topotecan/cyclophosphamide 1 (9) Cisplatin/ifosfamide 1 (9) VAC/IE 1 (9) IE 1 (9) Irinotecan/temozolomide 1 (9) Carboplatin/paclitaxel 1 (9) Radiation therapy Whole abdominal 4 (21) Palliative 1 (5) None 14 (74) Surgery Yes 11 (58) No 8 (42) Hyperthermic intraperitoneal chemotherapy Yes 5 (26) No 14 (74)