Clinical Characteristics, Management, and Outcomes of 19 Nonpediatric Patients with Desmoplastic Small Round Cell Tumor: A Cohort of Brazilian Patients

Table 2

Treatment modalities.

Treatment modality	Number of patients (%)
Chemotherapy
Neoadjuvant	9 (47)
Palliative	10 (53)
First line (n = 19)
VAC/IE	7 (37)
VAC	3 (16)
VAI	3 (16)
VAC/ICE	1 (5)
AI	1 (5)
Carboplatin/ifosfamide/etoposide	1 (5)
Carboplatin/paclitaxel/bevacizumab	1 (5)
Carboplatin/paclitaxel	1 (5)
Cisplatin/etoposide	1 (5)
Second line (n = 13)
IE	3 (23)
VAC	2 (15)
Pazopanib	2 (15)
High-dose ifosfamide	1 (7)
Dacarbazine/gemcitabine	1 (7)
Topotecan	1 (7)
Irinotecan	1 (7)
Sunitinib	1 (7)
FOLFOX	1 (7)
Third line (n = 11)
Gemcitabine/docetaxel	3 (27)
Irinotecan	2 (18)
Topotecan/cyclophosphamide	1 (9)
Cisplatin/ifosfamide	1 (9)
VAC/IE	1 (9)
IE	1 (9)
Irinotecan/temozolomide	1 (9)
Carboplatin/paclitaxel	1 (9)
Radiation therapy
Whole abdominal	4 (21)
Palliative	1 (5)
None	14 (74)
Surgery
Yes	11 (58)
No	8 (42)
Hyperthermic intraperitoneal chemotherapy
Yes	5 (26)
No	14 (74)