Review Article

Congenital Malformations of the Eye: A Pictorial Review and Clinico-Radiological Correlations

Figure 9

Congenital cataract and pseudophakia. Congenital cataract in a one-month-old girl (a). MRI axial T2WI (b) and postcontrast axial FS T1WI (c) of a three-month-old girl with bilateral cataracts. In the left eye, the cataract appears as a thickened crystalline lens, hyperintense both on T2WI and T1WI (black dotted arrow in (b) white dotted arrow in (c)). In the right eye, a cataract was treated, and an intraocular lens was placed: this apparent absence of the lens is called pseudophakia (black arrow in (b) white arrow in (c)). Axial DRIVE (d) and sagittal postcontrast T1WI (e) of a two-year-old patient affected by bilateral congenital cataract, secondary to galactosemia. In both eyes, the cataracts were treated and intraocular lenses were implanted, hence showing a pseudophakic appearance (black arrows in (d) white arrow in (e)).