Ehlers-Danlos Syndrome, Hypermobility Type: An Underdiagnosed Hereditary Connective Tissue Disorder with Mucocutaneous, Articular, and Systemic Manifestations

Table 7

The Beighton score for assessing generalized JHM.

Sign	Yes	No
Passive apposition of the right thumb to the flexor aspect of the forearm	1	0
Passive apposition of the left thumb to the flexor aspect of the forearm	1	0
Passive dorsiflexion of the right V finger beyond 90 degrees	1	0
Passive dorsiflexion of the left V finger beyond 90 degrees	1	0
Hyperextension of the right elbow beyond 190 degrees	1	0
Hyperextension of the left elbow beyond 190 degrees	1	0
Hyperextension of the right knee beyond 190 degrees	1	0
Hyperextension of the left knee beyond 190 degrees	1	0
Forward flexion of the trunk with the knees extended and the palms resting flat on the floor	1	0

Adapted from [10].
Note: the Beighton score ranges from 0 to 9. Generalized joint hypermobility is fixed for a total score of 5/9 or above for the Villefranche criteria and 4/9 or above for the Brighton criteria. Unstandardized modifications for specific population subgroups, such as children (increasing by 1 point these limits) and males (reducing by 1 point these limits), are reasonable. For noncollaborative subjects, a modified Beighton score lacking the spinal bending maneuver and a maximum score of 8 may be applied.