Research Article

Progressive Familial Intrahepatic Cholestasis: A Descriptive Study in a Tertiary Care Center

Table 4

Typical histological findings seen in PFIC types.

PFIC typeType 1Type 2Type 3Type 4

Histological featuresPeriportal and pericentrilobular fibrosisCanalicular cholestasis, portal inflammation, and fibrosis with giant cellsPortal inflammation, portal fibrosis, cholestasis, ductal proliferationBland cholestasis, hepatic necrosis, ductal proliferation, portal fibrosis