Review Article
IgG4 Cholangiopathy
Table 1
Disease spectrum of IgG4 pancreato-cholangiopathy and differential diagnosis.
| IgG4-related pancreato-cholangiopathy | Differential diagnosis |
| Autoimmune pancreatitis without bile duct involvement | Pancreatic cancer | Autoimmune pancreatitis with IgG4 cholangitis | Pancreatic cancer and cholangiocarcinoma | IgG4-related sclerosing cholangitis | Primary sclerosing cholangitis | IgG4-related sclerosing cholangitis with hilar pseudotumor | Hilar cholangiocarcinoma |
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