Review Article

IgG4 Cholangiopathy

Table 1

Disease spectrum of IgG4 pancreato-cholangiopathy and differential diagnosis.

IgG4-related pancreato-cholangiopathyDifferential diagnosis

Autoimmune pancreatitis without bile duct involvementPancreatic cancer
Autoimmune pancreatitis with IgG4 cholangitisPancreatic cancer and cholangiocarcinoma
IgG4-related sclerosing cholangitisPrimary sclerosing cholangitis
IgG4-related sclerosing cholangitis with hilar pseudotumorHilar cholangiocarcinoma