Case Report

Living Donor Liver Transplantation for Hepatic Venoocclusive Disease/Sinusoidal Obstruction Syndrome Originating from Hematopoietic Stem Cell Transplantation

Table 1

Data of previous reports on liver transplantation for VOD/SOS originating from HSCT.

LT typeAge/sexConditioning regimensTime to LT (day)Follow-up period statusCause of death

Case 1 (11)Deceased55/FCY/BU4254 daysDeathInfection
Case 2 (12)Deceased49/MCY/BU3131 daysDeathMOF
Case 3 (13)Deceased47/MCY/BU4160 daysDeathInfection/MOF
Case 4 (14)Deceased43/MEtoposide/CY/carmustine22/44(1st/2nd)70 daysDeathPneumonia, ARDS/TTP
Case 5 (13)Deceased39/FCY/BU7962 daysDeathAspergillosis/intracerebral hemorrhage/MOF
Case 6 (15)Deceased38/MCY/BU238 yearsAlive
Case 7 (16)Deceased35/MCY/TBI439 monthsAlive
Case 8 (17)Deceased34/FCY/BU211 yearAlive
Case 9 (18)Deceased34/FCY/BU3542 daysDeathInterstitial pneumonitis/MOF
Case 10 (19)Deceased33/MCY/BU363 daysDeathCerebral edema
Case 11 (19)Deceased32/FCY/TBI3930 daysDeathPneumonia
Case 12 (19)Deceased31/FCY/BU25213 daysDeathLiver failure
Case 13 (20)Deceased25/MCY/BU326 monthsDeathPneumocystis pneumonia
Case 14 (21)Deceased23/MCY/BU80140 daysDeathInfection
Case 15 (22)Living2 m/FCY/TBI339 monthsAlive
Case 16 (23)Living1/FCY/BU8429 monthsAlive
Case 17 (10)Living11 m/MCY/BU/TBI4217 monthsAlive
Our caseLiving16/FCY/etoposide/TBI84119 daysDeathSepsis/MOF

LT: Liver transplantation; Cy: Cyclophosphamide; BU: Busulfan; TBI: Total body irradiation; MOF: Multiorgan failure; ARDS: Acute respiratory distress syndrome; TTP: Thrombotic thrombocytopenic purpura.