Cardiac Epithelioid PEComa: Report of Two Cases and Review of the Literature

Table 4

Summary of clinicopathologic features of 7 reported cardiac PEComas.

Case	Age	Sex	TSC	Site	Size (cm)	Morphology	Mitosis/50 HPF	Atypical mitosis	Necrosis	Followup (month)
1 [14]	48	F	No	Rt atrium	6	Mixed vessels, smooth muscle, and fat	No	No	No	A&W, 20
2 [15]	38	F	No	Rt atrium	34	Mixed vessels, smooth muscle, and fat	Rare	—	—	Died, 9 days post-op
3 [10]	29	M	—	Lt atrium	12	Epithelioid cells	45	Yes	Yes	Died, post-op (not tumor related)
4 [16]	20	M	—	Pericardium	15	Epithelioid cells	>1	NA	Yes	A&W, 6
5 [17]	10	F	No	Lt atrioventricular groove	6	Spindle and epithelioid cells with bland nuclei	Rare	—	No	A&W, 18
6*	2	F	No	Lt atrium	6	Epithelioid cells	25/HPF	No	Yes	A&W, 32
7*	33	F	No	Lt atrium	NA	Epitheliod cells	46/HPF	Yes	Yes	AWD, 36

A&W: alive and well; post-op: postoperation; AWD: alive with disease; *: our cases.