Case Report

VEXAS Syndrome in a Patient with Myeloproliferative Neoplasia

Table 1

Organ manifestations of VEXAS syndrome in the present patient.

Organ systemsManifestations

SkinMigrating exanthem
Maculopapular rash

MusculoskeletalStiffness and pain
Edematous changes shown on CT scan

CirculationCerebral infarction
Pulmonary embolism

Bone marrowChanges correlating to ET
Vacuolization of myeloid and erythroid cells

ImmunologicalFever and night sweats
Increase in CRP