Case Report
“A Dangerous Black Box:” Idiopathic Hemophagocytic Lymphohistiocytosis in Adult Patients—A Case Report and Review of the Literature
| Known underlying immunodepression | No | Maximal temperature (°C) | Strictly greater than 39.4 | Hepatomegaly | No | Splenomegaly | Yes | Lower hemoglobin level | Strictly greater than 92 g/L | Lower leukocyte count | Less than or equal to 5 g/L | Lower platelet count | Less than or equal to 110 g/L | Higher ferritin level (ng/ml) | Strictly greater than 6000 | Higher triglyceride level (mmol/l) | Between 1.5 and 4 | Lower fibrinogen level (g/L) | Strictly greater than 2.5 | Higher ASAT/ALAT level (UI/l) | Greater than or equal to 30 | Hemophagocytosis features on the bone marrow aspirate | No | | Calculate | HScore | 209 | Probability of having HS (%) | 92.87735027549559 |
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